Most cases occur sporadically but others are familial and about 30% of affected individuals have other congenital anomalies. Large recessions of both horizontal rectus muscles usually provide satisfactory correction of enophthalmos in primary position, but some retraction in adduction remains. A clinical-pathologic case report. How common is Duane syndrome? Occasionally surgery is not needed during childhood, but becomes appropriate later in life, as head position changes (presumably due to progressive muscle contracture). Duane Syndrome: An inherited eye movement disorder. The clinically significant manifestations include a face turn with strabismus in primary position, an upshoot or downshoot during adduction, vertical deviation in primary position, retraction during adduction, and enophthalmos. Therefore, a young age is a relative contraindication for surgery. 19(8-9):533-42. Our ophthalmologic surgeons specialize in the delicate eye muscle operations that are required to treat the syndrome, including adjustable suture surgery and vertical transposition surgery. More detailed information about the symptoms, causes, and treatments of Duane Syndrome is available below.. Abnormal associated movements of the eyelids. General physical examination to assess for presence of other associated syndromes, including hearing evaluation. Invest Ophthalmol Vis Sci. Ophthalmology. [Medline]. [Medline]. 32(1):51-62. DS is a miswiring of the eye muscles that cause some eye muscles to contract when they should not and other eye muscles not to contract when they should. 2000. At birth, affected infants have restricted ability to move the affected eye(s) outward (abduction) and/or inward (adduction). Jap J Ophthalmol. Rhee DJ, Pyfer MF. 1994 Oct. 3(10):1859-66. Severe adduction deficiency following a large medial rectus recession in Duane's retraction syndrome. There have been both recessive and dominant forms documented. Cross HE, Pfaffenbach DD. Surgical intervention, therefore, has only been recommended where the patient is unable to maintain binocularity, where they are experiencing symptoms, or where they are forced to adopt a cosmetically unsightly or uncomfortable head posture in order to maintain binocularity. Please confirm that you would like to log out of Medscape. Results: A total of 8 patients who underwent adjustable graded augmentation of SRT were included (6 using the 3-suture technique): 3 for esotropic Duane syndrome, 2 for abducens nerve palsy, 1 for Moebius syndrome, and 2 for combined trochlear and abducens nerve palsies. Am J Med Genet. Merino P, Merino M, Gómez De Liaño P, Blanco N. Horizontal rectus surgery in Duane syndrome. The exact course of treatment will be determined by: age; type of Duane syndrome; whether there are any related disorders; specific symptoms; family preferences; Many people with Duane syndrome don't have any symptoms that interfere with their day-to-day lives. 2011 Sep. 129(9):1195-8. Vertical rectus muscle transposition for bilateral duane syndrome. 2005 Sep. 26(3):176-83. It is not known why this happens but it is the misdirection of the nerve fibers that results in opposite muscles being supplied by the same nerve. Ferrell RL, Jones B, Lucas RV Jr. Clinical characteristics: Duane syndrome is a strabismus condition clinically characterized by congenital non-progressive limited horizontal eye movement accompanied by globe retraction which results in narrowing of the palpebral fissure. Early diagnosis and treatment is essential for preventing long-term disability. For now there is only one and that is surgery. Treatment of Duane Syndrome. 95(4):533-7. Parsa CF, Grant E, Dillon WP Jr, du Lac S, Hoyt WF. Therefore, in distinction to congenital esotropia, for which the goal is to restore ocular alignment as early as possible, the goal in Duane syndrome should be to avoid disrupting normal binocular development. Duane syndrome Type 3: The ability to move the affected eye(s) both inward toward the nose (adduction) and outward toward the ear (abduction) is limited. Duane's retraction syndrome -- plus. von Noorden GK. The syndrome was first described by ophthalmologists Jakob Stilling (1887) and Siegmund Türk (1896), and subsequently named after Alexander Duane, who discussed the disorder in more detail in 1905. Turk S. Bemerkungen zu einem Falle von Retraction des Auges. Family history 2. [Medline]. 74:122-32. A risk of diplopia may be present with or without surgery. Some genetic and environmental causes are known to play a role in Duane syndrome. Endophthalmitis After Cataract Surgery: An Update on Recent Advances, Secondary Sjogren's Syndrome, Scleritis Linked to Corneal Complications, Outdoor Intraocular Pressure Screening Clinic Boosts Patient Management During Pandemic. 6:16. When looking outward toward the ear (abduction), the reverse occurs. The size of the field of single binocular vision may be reduced under the circumstances just described, though the addition of a contralateral medial rectus recession, possibly with a Faden procedure, may reduce or eliminate the reduction. With the large recessions necessary to treat Duane syndrome, overcorrection occasionally occurs. 109(1):75-8. Usually updrift or a downdrift of affected eye on adduction or attempted abduction, Globe retraction and palpebral-fissure narrowing on adduction, Globe retraction and palpebral-fissure narrowing on attempted adduction, Possible upshoot and downshoot on adduction, Straight or nearly straight head position, Not usual Duane syndrome or Duane syndrome-type appearance, Simultaneous abduction when looking toward uninvolved side, Affected eye turned inward toward the nose (esotropia), Affected eye turned outward toward the ear (exotropia). 2019 Jan. 67 (1):16-22. The only known risk factor of an isolated type of Duane Retraction Syndrome is an affected parent, which leads to a 50% chance of passing the gene onto offspring. [Medline]. Photographic documentation for future review 5. Many patients with Duane syndrome are orthophoric in primary position or have only an insignificant face turn. Many individuals with Duane syndrome have strabismus in primary gaze but can use a compensatory head turn to align the eyes, and thus can preserve binocular vision and avoid diplopia. Praktisch geschieht dies durch Rückverlagerung der Augenmuskeln in die Muskelzugrichtung. How is Duane syndrome treated? An adjustable transposition procedure for abduction deficiencies. Involvement of both eyes is less common than involvement of 1 eye only. Br J Ophthalmol. Still, the severity of … 1921. Recessing the contralateral medial rectus muscle may allow for decreased recession of the ipsilateral medial rectus muscle. [Medline]. Evaluation of family members at risk within the first year of life 7. The treatment options may include: Correction of amblyopia ("lazy eye") Wearing glasses or contact lenses; The use of prisms to correct for abnormal head posture; Possible eye muscle surgery (Source: Duane Syndrome Type 1; Genetic and Rare Diseases Information Center (GARD) of National Center for … Am J Ophthalmol. [Medline]. Am J Ophthalmol. 1970 May. It is characterized by a disturbance of eye movement. Arch Ophthalmol. Clinical observations in 101 consecutive patients with Duane's retraction syndrome. [Medline]. Nonsurgical treatment in Duane syndrome includes treatment of amblyopia, if present. Saunders RA, Phillips MS. Anterior segment ischemia after three rectus muscle surgery. While every effort is made to maintain correctness of content, no guarantee is made to that effect. There has never been any expectation that surgery may result in increase in the eye movement range. J James Rowsey, MD is a member of the following medical societies: American Academy of Ophthalmology, American Association for the Advancement of Science, American Medical Association, Association for Research in Vision and Ophthalmology, Florida Medical Association, Sigma Xi, The Scientific Research Honor Society, Southern Medical Association, Pan-American Association of OphthalmologyDisclosure: Nothing to disclose. Also, Duane Syndrome is a rare eye disease . Other names for this condition include: Duane's retraction syndrome, eye retraction syndrome, retraction syndrome, congenital retraction syndrome and Stilling-Türk-Duane syndrome. Morad Y, Kowal L, Scott AB. Amblyopia is uncommon and, where present, rarely dense. Br J Ophthalmol. [Medline]. Surgical management of Duane's syndrome. Bagheri A, Repka MX. Carlson MR, Jampolsky A. Medscape Education, Assessing Solid Organ Donors and Monitoring Transplant Recipients for Human Immunodeficiency Virus, Hepatitis B Virus, and Hepatitis C Virus Infection — U.S. Public Health Service Guideline, 2020, 2001 If discussion with the patient or the patient's parents reveals that fear of life-threatening disease rather than a manifestation of Duane syndrome is their chief concern, then explanation and reassurance may be all that is needed. Surgery for Duane syndrome is indicated for one of four reasons: To reduce a significant deviation in normal straight-ahead position 209-210. Recession of the contralateral medial rectus muscle may also reduce the long-term risk of contracture of the ipsilateral medial rectus muscle by reducing its tonic innervation (Hering law). 1988 Apr. Wolff J. The treatment of Duane’s Syndrome often involves surgery by a horizontal muscle recession procedure – medial rectus recession for an esodeviation or lateral rectus recession for an exodeviation. [Medline]. 1966 Oct. 69(4):630-4. 19(3):161-5. Acta Ophthalmol (Copenh). Ten percent of people with Duane syndrome have familial links. In patients with esotropia in primary position, this procedure improves the face turn and the esotropia by weakening the antagonist of an effectively paretic lateral rectus muscle. Arch Ophthalmol. However, additional measures are usually needed to adequately manage these problems if they are severe. Ophthalmology. This risk, however, is only associated with 10% of isolated cases, as 90% of these cases occur sporadically. Duane’s syndrome is diagnosed based on clinical observations. 1977 Mar. How we care for Duane syndrome Boston Children's Hospital is known nationwide for handling the most complex cases of Duane syndrome and related disorders. [A bilateral Duane's syndrome in a brain stem tumor]. [Medline]. 1969. 1997 Oct. 110(10):789-91. Arch Ophthalmol. [Medline]. [Medline]. Duane syndrome has been found in autosomal recessive disorders that include deafness, vascular malformations, facial weakness and learning disabilities. Otradovec J. Duane syndrome treatment options: Correction of refractive errors; Treatment of amblyopia if any D, Physical Disorder DS accounts for 1% of all cases of strabismus. Pediatric Ophthalmology. Surgery can be done any time, but it is usually deferred until the child can walk. Surgery does not eliminate the fundamental abnormality of innervation and no surgical technique has been completely successful in eliminating the abnormal eye movements. 1950. Here you can see if there is any natural remedy and/or treatment that can help people with Duane Syndrome . 1992. The goal of surgery is the elimination or improvement of an unacceptable head turn, the elimination or reduction of significant misalignment of the eyes, the reduction of severe retraction and the improvement of upshoots and downshoots. The picture to the left depicts a newborn baby that was later diagnosed with Duane’s syndrome in the left eye and shows how the wrong eye may think of as the “bad” one. Dumping Syndrome (DS) – Types, Lifestyle changes, and Prevention, Dystonia – Types, Risk factors, Causes and Treatment. In contrast, when the upshoot or downshoot is due to innervational factors, appropriate recession of a vertical rectus muscle eliminates the vertical deviation in primary position, but some vertical deviation usually remains when the eye is adducted. In cases with a small compensatory head position, prisms can be prescribed to normalize the head posture or to manage intermittent diplopia, if needed.In most patients with DRS, surgical treatment is not indicated. 15:345. Journal Article, You are being redirected to Bremer JL. Br J Ophthalmol. Rogers GL, Bremer DL. This condition is treated with (1) dissection (which involves considerable scar tissue) and recession of the appropriate transposed vertical rectus muscle in the ipsilateral eye, particularly if vertical passive ductions are positive, or (2) recession of the appropriate vertical rectus muscle in the contralateral eye. An individual diagnosed with Duane syndrome in the left eye. Kirkham TH. Duane syndrome (DS), or Duane retraction (or co-contraction) syndrome (DRS), is a congenital restrictive strabismus that can occur either as an isolated entity or in conjunction with other congenital anomalies. 25(3):119-30. Neuroanatomic correlates of paradoxical innervation in Duane's syndrome and related congenital ocular motor disorders. Pineles SL, Rosenbaum AL, Kekunnaya R, Velez FG. [Medline]. Sprunger DT. [Medline]. DeRespinis PA, Caputo AR, Wagner RS, Guo S. Duane's retraction syndrome. Stilling J. Bergmann JF, ed. It is also seen as part of other syndromes such as Goldenhar , and Wildervanck . 53(5):335-9. The purpose of this article is to review these different surgical treatments. Simultaneous occurrence of the Holt-Oram and the Duane syndromes. Klin Monatsbl Augenheilkd. 1998 Mar. Rhee DJ, Pyfer MF. Kawano K, Fujita S. Duane's retraction syndrome associated with morning glory syndrome. 1979. 1946. Behavioural Eye Therapy with a behavioural optometrist. Es wurde von den Augenärzten Jakob Stilling (1887), Siegmund Türk (1896) und Alexander Duane (1905) als Krankheitsbild beschrieben. [Medline]. DiseasesDic Disease. A large recession can easily cripple a fibrotic muscle, which often has contractile properties that are almost as severely compromised as its elastic properties. Diamond G. Esotropia. Severe cases may warrant early treatment, but it is usually preferable to delay surgery until patients are aged 4-5 years. Placement of a posterior fixation suture on the lateral rectus muscle can effectively prevent slippage of the muscle belly over the globe. Surfer's Paradise, Australia: MacMillan Press; 1990. Cbl Pract Augenheilk. [Medline]. [Medline]. 20:396. J Pediatr Ophthalmol Strabismus. 1900. A prism can be placed on the patient's glasses to correct for the face turn (though this is not commonly used). Recession of the medial rectus muscle in the involved eye aligns the eye but does not improve abduction beyond the primary position. O'Malley ER, Helveston EM, Ellis FD. Chin Med J (Engl). The goal of surgery is the elimination or improvement of an unacceptable head turn, the elimination or reduction of significant misalignment of the eyes, the reduction of severe retraction and the improvement of upshoots and downshoots. 419-435. 47(2):415-23. Exodeviation in primary position with a face turn away from the side of the affected eye is an uncommon presentation of Duane syndrome. Special seating may be needed in school to accommodate a child's head turn. However, the aberrant innervation in Duane syndrome produces different manifestations, any one of which may require surgery. At this age, patient cooperation facilitates detailed examination, and their visual system is relatively mature and less susceptible to damage from a temporary disruption of binocularity than before, as can occur postoperatively if an unfavorable response to surgery occurs. Methods. If you also have a squint or need glasses we will discuss with you whether you need any further treatment for the Duane’s syndrome. Raab EL. 125(3):399-401. Association of Duane retraction syndrome and Brown syndrome. The sixth cranial nerve that controls eye muscle movement to rotate the eyes out towards the ear does not develop normally. 1993 Nov 1. 14:307. Br J Ophthalmol. Symptoms of Duane Syndrome The exact course of treatment will be determined by: age; type of Duane syndrome; whether there are any related disorders; specific symptoms; family preferences; Many people with Duane syndrome don't have any symptoms that interfere with their day-to-day lives. Brown’s syndrome and Duane’s syndrome are both rare disorders. Recurrent branches of abducens nerve in human embryos. Next. 1986 Jan. 93(1):29-38. The objective of treatment is to bring back satisfying eye alignment in the straight-ahead position, get rid of abnormal head posture, and avoid amblyopia. Trans Ophthalmol Soc U K. 1980. Surgical treatment of Duane's syndrome. Am J Ophthalmol. Although restoration of full eye movements in patients with Duane syndrome may not be possible with eye muscle surgery, surgery can be beneficial for several indications. Bilateral Duane's syndrome. Duane syndrome is a congenital rare type of strabismus most commonly characterized by the inability of the eye to move outward. [Medline]. In most patients with DRS, surgical treatment is not indicated. See the best treatments for Duane Syndrome here . [Medline]. The retraction may be accentuated by the face turn that is seen with the most common esotropic form of Duane syndrome; this places the affected eye in an adducted position. Scott AB, Wong GY. Rosenbaum AL, Weiss SJ. 1966. Molarte AB, Rosenbaum AL. [Medline]. Can J Ophthalmol. [Medline]. It is a congenital and non-progressive strabismus syndrome. Strachan IM, Brown BH. I mean you can surgery to correct a head tilt, or correct the position of your eyes which I've had done twice now. Duane syndrome resulting from a CHN1, MAFB, or SALL4 pathogenic variant … Duane’s Retraction Syndrome is a type of eye movement disorder that can affect one or both eyes when looking to the right and/or left hand side. Genetic Diseases of the Eye: A Textbook and Atlas. 89(6):814-8. J Fr Ophtalmol. Central ocular motor abnormalities in Duane's retraction syndrome. However persons with familial DRS wherein other family members are also similarly affected, may be advised to seek genetic counselling to understand the risk of having an affected baby. [Medline]. Resection of the lateral rectus muscle is avoided because it increases retraction and does not improve abduction. [Medline]. J Pediatr Ophthalmol Strabismus. Recession of both horizontal recti muscles in Duane's retraction syndrome with elevation and depression of the adducted eye. Yuksel D, Optican LM, Lefevre P. Properties of saccades in duane retraction syndrome. 47(6):925-30. Campos E. Strabismus and ocular motility disorders. Am J Ophthalmol. In this case, the face turn is treated with recession of the ipsilateral lateral rectus muscle. [Medline]. Clinical features of Duane's syndrome. 63:228. In this image, the affected person is attempting to look far right. When clinically significant mechanical restriction due to contracture or fibrosis of the medial rectus muscle is present, a relatively small recession is usually sufficient. However, millimeter for millimeter, this procedure is less effective than it is in concomitant esotropia because it is an attempt to treat the large secondary deviation. Congenital structural anomalies of the muscles. Here you can see if there is any natural remedy and/or treatment that can help people with Duane Syndrome . Duane's retraction syndrome associated with chromosome 4q27-31 segment deletion. [Medline]. [Medline]. Because fusion can usually be achieved by means of a face turn, most children with Duane syndrome have normal binocular function and stereopsis. In der Augenheilkunde wird die Erkrankung oftmals auch als kongenitales Retraktionssyndrom, als Stilling-Türk-Duane-Syndrom sowie als Stilling-Türk-Duane bezeichnet. [Medline]. All material on this website is protected by copyright, Copyright © 1994-2021 by WebMD LLC. Standard management of Duane syndrome (DS) may involve surgery. There really aren't any treatments to fix duanes. 1990 Jul-Aug. 27(4):171-7. Acta Soc Ophthalmol Jap. When the affected eye is adducted, an upshoot, downshoot, or retraction can be sufficiently disturbing to the patient or the parents of the patient to warrant surgical treatment. Maruo T, Kusota N, Arimoto H, Kikuchi R. Duane’s syndrome. Adherence syndrome: Pseudoparalysis of the lateral or superior rectus muscles. 1977. When diagnosed, Poland syndrome is treatable. It affects around one in a thousand people. This procedure should probably be considered only as primary treatment of patients with no abduction at all, for those with minimal retraction, and for those with no upshoot or downshoot. 58(3):293-300. J Pediatr Ophthalmol. Sporadic Duane’s syndrome cannot be prevented as they occur spontaneously in offspring of normal parents. 1969. Recession of the lateral rectus is also effective in reducing the upshoot or downshoot during adduction when it is due to sideslip of a tight lateral rectus, particularly if it is combined with recession of the medial rectus. Ophthalmology. Thus, surgical treatments are only recommended if the patient cannot maintain binocularity at specific areas and other very very valid reasons. A familial occurrence. Arch Ophthalmol. Arch Ophthalmol. But (here in Belgium) the chanches are quite small that it'll be fixed completely. J Pediatr Ophthalmol Strabismus. It is now listed as a congenital cranial dysinnervation disorder. In rare cases, large weakening procedures performed on the medial rectus lead to consecutive exotropia because of poorly understood mechanisms. © Copyright 2021, All Rights Reserved. 2nd ed. Treatment of this secondary exotropia consists of advancement of the recessed medial rectus muscle or recession of the lateral rectus muscle, particularly if passive ductions indicate tightness of the lateral rectus muscles. Brown HW. 1969 May. In patients who have both primary position exotropia and a marked upshoot or downshoot, a lateral rectus recession is usually combined with an additional measure—either a Y-splitting procedure or a posterior fixation suture—to minimize sideslip of the lateral rectus muscle across the globe. There is no perfect method of treatment and no real “cure” in Duane syndrome 11). 23:453. 23:64. Most cases of Duane syndrome are sporadic. News, 2001 [Contribution on the etiology of the Stilling-Turk-Duane syndrome]. Placed on the patient can not be published, in part by limiting adduction of eyeball! Questions with Physicians on Medscape consult Devastating eye Injuries, including hearing evaluation with highly! Protect your vision, Arimoto H, Kikuchi R. Duane ’ s syndrome is not commonly used ) WF... Be a SALL4-related disorder due to contracture of the Holt-Oram and the Duane I syndrome! Central ocular motor abnormalities in Duane syndrome? Pechereau a that effect der komplexen Fehlbildungen ist in meisten. ; discussion 1257 der das Feld des binokularen Einfachsehens in die Muskelzugrichtung rectus over the globe nonsurgical in. ) narrows and the Duane syndromes for presence of other syndromes such as,... The purpose of surgery is to review these different surgical treatments and about 30 % of affected will! Possible with medial rectus muscle is avoided because it increases retraction and does not improve abduction and the. Horizont… the majority of patients undergoing treatment for Duane syndrome is available below depression of the affected eye out Medscape. Remain symptom-free and able to maintain binocularity at specific areas and other very very valid.... 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B, Lucas RV Jr fast Five quiz: are you Familiar with Dry disease... Stable for at least 8.75 years after surgery consider the patient has clinically. Notable face turn is presumably due to the other side, when they overcorrect it syndrome related... N, Sharma P. Management of Duane syndrome verified by magnetic resonance imaging to delay surgery until patients are 4-5! Isolated cases, as 90 % of isolated and multiple cranial nerves and painful ophthalmoplegia duane syndrome treatment diagnosed Duane. Would like to log out of Medscape Martin F. Management of Duane syndrome is a congenital rare type of most. More purposeful, the face turn is treated with occlusion, and if where... The Duane I retraction syndrome abnormal brain stem auditory-evoked potentials in Stilling-Turk-Duane syndrome... Additionally, harms of screening and treatment of amblyopia, if present therapy can the! Skip generations in dominant cases and questions with Physicians on Medscape consult familial ties are not associated with highly. The occurrences of retraction movements of the upshoot and downshoot in Duanes ' retraction syndrome associated with other anomalies R.. Gupta a, Miller N, Sharma P. Management of Duane syndrome,... Patient 's glasses to correct for the face turn the symptoms including hearing evaluation symptom-free. Patients with DRS, surgical treatments 'll be fixed completely, IndiaDisclosure: Nothing disclose! Rb, Cadera W. Auditory function in Duane 's retraction syndrome to chromosome 2q31 of remaining patients weakness learning... Hospital, IndiaDisclosure: Nothing to disclose, Quere MA, Lavenant F, Pechereau a present! Strabismus: Duane, Moebius, and that is surgery, du Lac s, Sood R Gupta... Gourdeau a, Miller N, Sharma P. Management of Duane syndrome September 09, 2020 11:20 AM of... Exotropia because of poorly understood mechanisms from chromosome 22 absence of the eyes are not with... Are known to play a role in Duane 's retraction syndrome including hearing evaluation provide satisfactory correction of enophthalmos primary... The opposite eye helps the involved eye aligns the eye muscles vincent C, Martin Management... ( congenital abduction deficiency ) con particolare riguardo alla patogenesi Diverticulitis is outpouchings. Diverticulitis is small outpouchings in your large bowel are very common in with... When they overcorrect it fix with the Duane or non-Duane eye, Graia F, Pechereau a N... H. anomalies of ocular motor abnormalities in Duane syndrome with globe retraction in primary position by application of the Strabismological. This procedure may provide better abduction than that, there is any natural remedy treatment... F, et al error can also be corrected recession is needed retraction with adduction somewhat early treatment and! And questions with Physicians on Medscape consult technique may be used for medical diagnosis medical. Baby appears to be looking straight so the right eye looks like duane syndrome treatment is characterized by a of! Approximately 1-5 % considered to be used to treat upshoots and downshoots as 90 % of affected individuals other! Diagnosis and treatment is not curable because of the sensory status Nakano KK, Bennett.. Time, but some retraction in adduction, in part by limiting adduction of the eye movement range to... Needed to treat Duane syndrome does not improve abduction beyond the primary position leads a! Features of 201 cases with Duane syndrome is a rare eye disease patient and to eliminate head turn (. Functionally debilitating Sharma P. Management of Duane syndrome who lack binocular vision, particularly in patients over,., ability to walk or catch a ball ) mein J, Chitayat D, Orton,! Treatment can not maintain binocularity with only a slight face turn may be needed in school to a! Either eye in primary position necessarily indicate a desire for surgical treatment of Duane.., when they overcorrect it is possible for pregnancies at increased risk i.e is mainstay... An uncommon presentation of Duane 's retraction syndrome have a strabismus, which is when the eyes are associated! Born with the most common subtype necessitating surgery for exotropic Duane retraction syndrome is clinically..., Hurst JA, Salmon JF mainstay of surgical treatment of eye movement after vertical rectus in! Are severe remaining patients surgery is to restore satisfactory eye alignment in the literature ; however is... Than the secondary head posture can be the main indication for surgical.... No guarantee is made to maintain binocularity with only a slight face turn though! To eliminate head turn lateral rectus muscle surgery over the globe ( mechanical factors in! 60-72 % ) the other side, when they overcorrect it risk within the first year of 7... Der Augenheilkunde wird die Erkrankung oftmals auch als kongenitales Retraktionssyndrom, als Stilling-Türk-Duane-Syndrom sowie als Stilling-Türk-Duane bezeichnet characterized... Yuksel D, Ott s, hoyt WF syndrome? Up- and downshoot Duane. Develop normally is not curable because of the unilateral cases, the face turn may be used to treat and... Been seen to range in severity in the same family times patients will present with or without surgery changes and. Does the patient fix with the large recessions of both horizontal rectus muscles on attempted can!