Type 1 and Type 2. Indian J Pediatr. Long segment bony spur in split cord malformation Type 1. Sometimes there is only one protective membrane or sleeve (the dura) around both parts of the spinal cord. 2017. L5 and S1), split cord malformation type I which separated two hemi-cords, tethered cord and syringomyelia. 13. Compared with Type II SCM, patients with Type I SCM presented with higher incidence of kyphotic deformity, more extensive and complicated vertebral anomalies, and more complex rib anomalies. Neurosurgery. The complete or partial division of the spinal cord is due to the presence of a septum in the central part of the spinal canal. Defined as two hemicords, each with its own central canal and surrounding pia, each within a separate dural tube separated by a dural-sheathed rigid osseocartilaginous (bony) median septum. There was a bony spur arising from the D 11 body level without a separate dural covering but with 2 cords. There were more type I (n = 22) than type II (n = 15) SCM. MahapatraAn unusual case of 4 level spinal dysraphism: multiple composite type 1 and type 2 split cord malformation, dorsal myelocystocele and hydrocephalous. The presence of bony spurs seen in type 1 SCM are usually partial and unequivocally are found attached to the dorsal surface of the vertebral body. Chiari malformation type 1 is a structural abnormality of the cerebellum, the part of the brain that controls balance, and the skull. Age, gender, symptoms and signs, radiological and operative findings, complications, associated anomalies, outcome, and pathological specimens were analyzed. Often, the split is caused by a thin segment of bone or cartilage that protrudes from the spinal column into the spinal cord space. Background: Split cord malformation (SCM) remains an important cause of tethered cord syndrome. This has often (but not consistently) been referred to as diastematomyelia. These images are from the case of a 29-yr-old woman with back pain without neurological symptoms. In SSCM Type I, each spinal cord has its own dura tube. DIASTEMATOMYELIA or split cord malformation is a rare phenomenon that may be discovered on magnetic resonance imaging of the spine. The split spinal cord malformation (SSCM) is an uncommon congenital malformation of the vertebral canal in which parts of the spinal cord are longitudinally duplicated. 1992 Sep;31(3):451-80. Rev Neurol (Paris). Guilloton L, Allary M, Jacquin O, Billaud Y, Drouet A, Felten D. Split-cord malformation (diastematolmyelia) presenting in two adults: Case report and a review of the literature. Split cord malformation (diastematomyelia): a complex type of spinal dysraphism in which the spinal cord splits lengthwise into two distinct cords. Type 1 and Type 2. Whereas, in Type II split cord malformations both the hemicords lie withina single, non-duplicated, dural tube[2]. Type I split cord malformation References [1] Pang D, Dias MS, Ahab-Barmada M. Split cord malformation: Part I: A unified theory of embryogenesis for double spinal cord malformations. Diastematomyelia: a type 1 split spinal cord malformation. We report the rare finding of a split cord malformation in a young girl. Beuriat PA(1), Di Rocco F(1), Szathmari A(1), Mottolese C(2). There was no hydrocephalus. A Type I SCM consists of two hemicords, each contained within its own dural tube and separated by a dura-sheathed rigid osseocartilaginous median septum. Split spinal cord malformation Synonyms: Diastematomyelia, SSCM, Diplomyelia, Pseudodiplomyelia, Dimyelia, Split cord malformation, SCM type 1, Split cord malformation type 1 Back to top With split cord malformation ( SCM ) for all double spinal cord with or without a bony spur separates two., both parts of the cord extended from D 5 to D 11 level dorsal myelocystocele and.! 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